Nipple shaped solitary nevus lipomatosus cutaneous superficialis: Report of a case and a review of the Korean literatures

Nevus lipomatosus cutaneous superficialis is a fairly uncommon form of connective tissue disorder, and this is characterized by the ectopic deposition of fat lobules in the dermis. There are two clinical variants: the multiple and solitary types. Particularly for the case of the solitary forms, it seems preferable to regard them instead as pedunculated lipofibromas. We report here on a case of a nipple shaped solitary nevus lipomatosus cutaneous superficialis, and we also review the Korean cases. Till now, 22 cases in Koreahave been reported as a solitary nevus lipomatosus cutaneous superficialis and a pedunculated lipofibroma, or both. The review of the Korean cases revealed that solitary nevus lipomatosus cutaneous superficialis almost always exhibits a single skin-colored dome shaped or pedunculated nodule on the thigh and buttock, as well as on the non-girdle area after the 4th decade, and it has no histopathological difference from the multiple forms.